TITLE:
Surgical Treatment of Tetralogy of Fallot with Pulmonary Valve Agenesis in a 22 Years Old Patient
AUTHORS:
Papa Salmane Ba, Kabulo Yannick, Momar Sokhna Diop, Papa Amath Diagne, Ndeye Fatou Sow, Papa Adama Dieng, Amadou Gabriel Ciss
KEYWORDS:
Tetralogy of Fallot, Pulmonary Valve Agenesis, Adult, Surgical Repair
JOURNAL NAME:
World Journal of Cardiovascular Surgery,
Vol.11 No.4,
April
15,
2021
ABSTRACT: Agenesis of pulmonary valve is a rare variant and severe form of Tetralogy of Fallot (ToF). The evolution is usually marked by respiratory and cardiac failure at early age, which needs early surgical correction. Uncorrected treatment of Tetralogy of Fallot diagnosed at adult age is infrequent and only few studies have been described. We present here a rare case of a 22 years old patient who presented with dyspnea since childhood. Subsequent investigations allowed diagnosis of treatment of Tetralogy of Fallot with agenesis of the pulmonary valve. Following the assessment, the patient underwent a surgical repair and the recovery was uneventful. The management of treatment of Tetralogy of Fallot with pulmonary valve agenesis in adult period remains complex, requiring different surgical techniques.