TITLE:
Ebstein Anomaly: A Clinical Case Series among Adolescents in Guinea
AUTHORS:
Mamadou Bassirou Bah, Elhadj Yaya Baldé, Mamadou Aliou Baldé, Thierno Siradjo Baldé, Mariama Djalakhan Diallo, Amadou Diouldé Doumbouya, Ibrahima Sory Sylla, Alpha Koné, Ibrahima Sory Barry, Souleymane Diakité, Sana Samoura, Mamadou Diallo, Abdoulaye Camara, Mamadou Dadhi Baldé
KEYWORDS:
Ebstein Anomaly, Adolescent, Congenital Heart Disease, Guinea
JOURNAL NAME:
World Journal of Cardiovascular Diseases,
Vol.13 No.4,
April
24,
2023
ABSTRACT: Ebstein’s anomaly is a rare congenital heart disease. We report a series of 4 cases of Ebstein’s anomaly discovered in adolescents. The mean age was13.75 ± 0.96,with3 boys and one girl. Three were in heart failure. The EKGshowed atrial hypertrophy (1 case), right bundle branch block (1 case),Wolff-Parkinson-White (1 case),andatrial fibrillation (1 case). Cardiomegalywas present in all patients with a mean cardiothoracic index of 0.77 ± 0.03.On echocardiography, the mean apical displacement of the tricuspid septalleaflet was 22.5 ± 3.30mm/m2, the Celermajer index was Grade 2 in 2 patients and Grade 4 in 2 patients. Depletive medical treatment was prescribedto3 patients. Anticoagulant therapy was initiated in one patient. Two are awaiting surgery. One death was recorded, it was at Grade 4 of the Celermajer index.